- 359.0 Congenital hereditary muscular dystrophy
- Autosomal dominant transmition, wide range of expression
- Often characterized by weakness and impaired shoulder funtion. Muscle involvement is diffuse, but the deltoid muscle is usually spared.
- Scapular winging often results. Scapulathoracic fusion improves upper extremity function.
- Atasoy E, JBJS 2000;82Br;813
- Bunch WH, JBJS 1993;75A;372