You are here

Radial Longitudinal Deficiency 755.26

 

synonyms: radial club hand, radial dysplasia

Radial Longitudinal Deficiency ICD-9

  • 755.26 Longitudinal deficiency, radial, complete or partial

Radial Longitudinal Deficiency Etiology / Epidemiology / Natural History

  • Failure of formation of the radial side of the forearm, wrist and hand
  • Rare

Radial Longitudinal Deficiency Anatomy

  • Deficiencies in radial artery, median or radial nerves, frlexor carpi radialis

Radial Longitudinal Deficiency Clinical Evaluation

  • Elbow flexion contracture
  • Radial deviation of the wrist
  • Thumb aplasia/hypoplasia

Radial Longitudinal Deficiency Xray / Diagnositc Tests

  • A/P and lateral of forearm and wrist.

Radial Longitudinal Deficiency Classification / Treatment

  • Bayne I
    -delayed appearance of distal epiphysis and shortened radius
    -Treatment: stretching exercises, serial casting of splinting beginning shortly after birth.
  • Bayne II
    -deficient proximal and distal radial growth, very short radius
    -Treatment: stretching exercises, serial casting of splinting beginning shortly after birth. Consider progressive distraction lengthening (Sabharwal S, JPO 2005;25:377).
  • Bayne III
    -parital absence of the radius, geenerally distal
    -Treatment: centralization of the carpus done at 6-12 months of age. Consider index finger pollicization for patients with thumb hypoplasia (Goldfarb CA, J Hand Surg 2002;27A:118).
  • Bayne IV
    -radius completely absent
    -Treatment: centralization of the carpus done at 6-12 months of age. Consider index finger pollicization for patients with thumb hypoplasia (Goldfarb CA, J Hand Surg 2002;27A:118).

Radial Longitudinal Deficiency Associated Injuries / Differential Diagnosis

  • Thrombocytopenia-absent-radius
  • Fanconi's anemia
  • Holt-Oram syndrome
  • Vertebral-anal-cardiac-tracheal-esohpageal-renal-radial limb (VACTERRL) association.

Radial Longitudinal Deficiency Complications

  • Recurrent deformity
  • Limited hand function

Radial Longitudinal Deficiency Follow-up Care

Radial Longitudinal Deficiency Review References

  • Bayne LG, J Hand Surg 1987;12A:169
  • °